Primary biliary cirrhosis - Sanjay Manohar's Medical Browser
Primary biliary cirrhosis
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Synonyms
PBC
Causes
Sjogren syndrome
Rheumatoid disease
Diffuse systemic sclerosis
Anti-smooth muscle antibody
Renal tubule acidosis
Effects
Pruritus
Fatigue
Common bile duct obstruction
Portal hypertension
Pyoderma gangrenosum
Osteomalacia
Raised angiotensin converting enzyme
Mallory body
High liver copper
High IgM
Liver granuloma
Periportal granuloma
Periportal fibrosis
Non-caseating granuloma
Antimitochondrial antibody
Kayser-Fleischer ring
Parents
Autoimmune liver disease
Biliary cirrhosis
Treatments
Ursodeoxycholic acid
Cholestyramine
Rifampicin
Naloxone
Liver transplant
Description
"10:1 female:male ratio Presents at 40-60 yrs 20-fold risk of HCC 80% Sjogren 20% scleroderma 20% lung fibrosis 98% have AMA Survival 10 yrs (2 yrs with jaundice)"
Type item name:
Sanjay Manohar
2006