Behcet disease - Sanjay Manohar's Medical Browser
Behcet disease
external
Synonyms
Behcet's disease
Beh�et disease
Silk road disease
Causes
HLA-B5
HLA-B51
Turkish origin
Effects
Behcet triad
Uveitis
Retinal vasculitis
Pericarditis
Chronic abdominal pain
Diarrhoea
50.0%
Venous thrombosis
20.0%
Arterial thrombosis
Aortic regurgitation
Transverse myelitis
Erythema nodosum
Noninfective meningitis
Positive pathergy test
Antiphospholipid syndrome
Bulbar palsy
Migratory polyarthritis
Brainstem syndrome
Parents
Autoimmune disease
Treatments
Cyclosporin
Glucocorticoid
Description
"2:1 male preponderance
onset at 30 yrs. 30% have a family history prevalent in areas of the old silk trading routes in the Middle East & Central Asia. Hence sometimes known as Silk Road Disease. Mortality is usually low "
Type item name:
Sanjay Manohar
2006