Adrenal insufficiency alacrima and achalasia syndrome - Sanjay Manohar's Medical Browser
Adrenal insufficiency alacrima and achalasia syndrome
Synonyms
- Triple-A syndrome
- Quadruple-A syndrome
- Allgrove syndrome
- 4A syndrome
- Achalasia-Addisonianism-Alacrimia syndrome
- AAA syndrome
Effects
Parents
Description
- "rare autosomal recessive congenital disorder:
-adrenal insufficiency-Addison's disease due to ACTH resistance.
-alacrima -absence of tear secretion
-achalasia cardia"